Peutz-Jeghers syndrome with disappeared pigmentation on lips after operation: A case report
Keywords:
Hamartoma, intussusception, intestinal obstruction, lips, polyps, Peutz-Jeghers syndromeAbstract
Peutz-Jeghers polyps are hamartomas of the small bowel which occur as part of the Peutz-Jeghers syndrome, a rare autosomal dominant condition characterized by gastrointestinal polyps and mucocutaneous melanotic pigmentation. We, hereby, report a case of a young female suffering from this syndrome who presented with hyperpigmentation of the lips and acute intestinal obstruction due to intussusception. An exploratory laparotomy was performed which revealed jejuno-jejunal and jejuno-ileal intussusceptions for which resection and anastomosis was done. There were multiple intraluminal polyps in the jejunum which upon histopathological examination, showed features of Peutz-Jeghers polyp. But, on postoperative day 11, we found the pigmentation on her lips disappeared, the patient behaved well in the postoperative period.
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