Multiple primary GISTs: Unusual presentation as jejuno-jejunal intussusception
Keywords:
Multiple GISTs, jejuno-jejunal, CT, intussusceptionAbstract
Gastrointestinal stromal tumors (GISTs) are rare, occurring in 10 - 15 per million, and 0.2% of all gastrointestinal tumors, and is generally considered a solitary tumor. This study presented a 57 year-old female with abdominal pain and intermittent vomiting for 6 months. Acute abdomen series did not show any evidence of a small bowel obstruction. Esophagogastroduodenoscopy (EGD) suggested partial small bowel obstruction. A contrast enhanced CT scan (CECT) of the abdomen demonstrated jejuno-jejunal intussusception induced by an intraluminal tumor and another two mesenteric tumors confirmed by histopathology and immunohistochemistry as GISTs. The patient had complete resection for treatment. She recovered without complication and remained well. This study reported a rare case of multiple primary GISTs with unusual presentation as intussusception. CECT is able to detect tumors, their location, suggest diagnosis, and define complications and metastasis.
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